TY - CHAP
T1 - Arrhythmogenic cardiomyopathy
AU - Proost, Virginnio M.
AU - Wilde, Arthur A. M.
PY - 2020/9/21
Y1 - 2020/9/21
N2 - Electrocardiography (ECG) is a critically important modality in the investigation of patients with cardiomyopathy of any kind, including arrhythmogenic cardiomyopathies. In some specific arrhythmogenic cardiomyopathies, the ECG is to some extent diagnostic, e.g. QRS microvoltages in the extremity leads to PLN-associated cardiomyopathy and prolonged PQ interval with a narrow QRS in laminopathies. In others, it contributes to the diagnosis, e.g. an epsilon wave, negative T waves beyond V1-V2 and a prolonged terminal activation duration in V1 in arrhythmogenic right ventricular cardiomyopathy (ARVC). Most often, however, these ECG features exhibit high specificity by low sensitivity. Electrocardiographic features are also included in risk calculators, risk for future cardiac arrhythmic events, that have been described in recent years. An example of the latter is the number of precordial leads with negative T waves in ARVC.
AB - Electrocardiography (ECG) is a critically important modality in the investigation of patients with cardiomyopathy of any kind, including arrhythmogenic cardiomyopathies. In some specific arrhythmogenic cardiomyopathies, the ECG is to some extent diagnostic, e.g. QRS microvoltages in the extremity leads to PLN-associated cardiomyopathy and prolonged PQ interval with a narrow QRS in laminopathies. In others, it contributes to the diagnosis, e.g. an epsilon wave, negative T waves beyond V1-V2 and a prolonged terminal activation duration in V1 in arrhythmogenic right ventricular cardiomyopathy (ARVC). Most often, however, these ECG features exhibit high specificity by low sensitivity. Electrocardiographic features are also included in risk calculators, risk for future cardiac arrhythmic events, that have been described in recent years. An example of the latter is the number of precordial leads with negative T waves in ARVC.
UR - https://www.scopus.com/inward/record.uri?partnerID=HzOxMe3b&scp=85148918436&origin=inward
UR - https://www.ncbi.nlm.nih.gov/pubmed/36846087
U2 - https://doi.org/10.1007/978-3-030-52173-8_7
DO - https://doi.org/10.1007/978-3-030-52173-8_7
M3 - Chapter
C2 - 36846087
SN - 9783030521721
T3 - Electrocardiography of Inherited Arrhythmias and Cardiomyopathies: From Basic Science to Clinical Practice
SP - 85
EP - 115
BT - Electrocardiography of Inherited Arrhythmias and Cardiomyopathies: From Basic Science to Clinical Practice
A2 - Green, Martin
A2 - Krahn, Andrew
A2 - Alqarawi, Wael
PB - Springer International Publishing
CY - Cham, Switzerland
ER -