TY - JOUR
T1 - Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway
AU - Wanders, Ronald J. A.
AU - Duran, Marinus
AU - Loupatty, Ference J.
PY - 2012
Y1 - 2012
N2 - Valine is one of the three branched-chain amino acids which undergoes oxidation within mitochondria. In this paper, we describe the current state of knowledge with respect to the enzymology of the valine oxidation pathway and the different disorders affecting oxidation
AB - Valine is one of the three branched-chain amino acids which undergoes oxidation within mitochondria. In this paper, we describe the current state of knowledge with respect to the enzymology of the valine oxidation pathway and the different disorders affecting oxidation
U2 - https://doi.org/10.1007/s10545-010-9236-x
DO - https://doi.org/10.1007/s10545-010-9236-x
M3 - Article
C2 - 21104317
SN - 0141-8955
VL - 35
SP - 5
EP - 12
JO - Journal of Inherited Metabolic Disease
JF - Journal of Inherited Metabolic Disease
IS - 1
ER -