Segmental muscular atrophy of the distal upper extremity (Hirayama disease): An atypical case with anterior dural detachment

Research output: Contribution to journalArticleAcademicpeer-review

1 Citation (Scopus)


Segmental non-progressive spinal muscular atrophy of the upper extremity, also known as Hirayama disease (HD), is a disorder seen mainly in young male patients of Asian ancestry. On MRI loss-of-attachment between the posterior dural sac and adjacent lamina has been described as the only significantly important predictor of HD. We herein present a patient with HD who showed an atypical anterior detachment of the dura mater from the adjacent vertebral body.

Original languageEnglish
Pages (from-to)e53-e55
JournalEuropean Journal of Radiology Extra
Issue number2
Publication statusPublished - 1 Nov 2009


  • Cervical spine
  • Hirayama disease
  • Spinal muscular atrophy

Cite this