Abstract
Hirayama disease is a self-limiting cervical motor neuron disease, usually affecting the spinal cord at level C7-T1. We share an unusual case of Hirayama disease in a young man affecting roots C4-C6. He presented in coma due to diaphragm weakness and hypercapnic respiratory failure. Diagnosis was achieved via clinical presentation, neurophysiological examination, ultrasonography of the diaphragm and dynamic MR-imaging. Conservative treatment with a cervical collar resulted in remarkable improvement in respiratory and motor function.
Original language | English |
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Pages (from-to) | 272.e3-272.e5 |
Journal | American Journal of Emergency Medicine |
Volume | 76 |
Early online date | 2 Dec 2023 |
DOIs | |
Publication status | Published - 1 Feb 2024 |
Keywords
- Diaphragm weakness
- Hirayama disease
- Respiratory failure
- Ultrasonography, MR imaging