Chronic bullous disease of childhood and a paecilomyces lung infection in chronic granulomatous disease

J.H. Sillevis Smitt, J.H.W. Leusen, H.G. Stas, A.H. Teeuw, R.S. Weening

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Abstract

A 12 year old boy suffering from p67-phox deficient chronic granulomatous disease presented with a bullous skin disease and a lung infection with paecilomyces species. The histopathology of a bullous lesion showed subepidermal blister formation and microabcesses containing eosinophils in the dermal papillae. By direct immunofluorescence, linear staining of IgA at the dermal-epidermal junction was detected which confirmed the clinical diagnosis of chronic bullous disease of childhood (linear IgA dermatosis)
Original languageUndefined/Unknown
Pages (from-to)150-152
JournalArchives of disease in childhood
Volume77
Issue number2
DOIs
Publication statusPublished - 1997

Keywords

  • AMC wi-co
  • AMC wi-eigen

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