Abstract
A 12 year old boy suffering from p67-phox deficient chronic granulomatous disease presented with a bullous skin disease and a lung infection with paecilomyces species. The histopathology of a bullous lesion showed subepidermal blister formation and microabcesses containing eosinophils in the dermal papillae. By direct immunofluorescence, linear staining of IgA at the dermal-epidermal junction was detected which confirmed the clinical diagnosis of chronic bullous disease of childhood (linear IgA dermatosis)
Original language | Undefined/Unknown |
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Pages (from-to) | 150-152 |
Journal | Archives of disease in childhood |
Volume | 77 |
Issue number | 2 |
DOIs | |
Publication status | Published - 1997 |
Keywords
- AMC wi-co
- AMC wi-eigen