TY - JOUR
T1 - Surveillance of Fontan-associated liver disease
T2 - current standards and a proposal from the European Society of Paediatric Radiology Abdominal Task Force
AU - Perucca, Giulia
AU - de Lange, Charlotte
AU - Franchi-Abella, Stéphanie
AU - Napolitano, Marcello
AU - Riccabona, Michael
AU - Ključevšek, Damjana
AU - Toso, Seema
AU - Herrmann, Jochen
AU - Stafrace, Samuel
AU - Darge, Kassa
AU - Damasio, Maria Beatrice
AU - Bruno, Costanza
AU - Woźniak, Magdalena Maria
AU - Lobo, Luisa
AU - Ibe, Donald
AU - Smets, Anne M.
AU - Petit, Philippe
AU - Ording Müller, Lil-Sofie
N1 - Publisher Copyright: © 2021, The Author(s).
PY - 2021/12
Y1 - 2021/12
N2 - Since Francis Fontan first introduced the eponymous technique, the Fontan procedure, this type of surgical palliation has allowed thousands of children affected by specific heart malformations to reach adulthood. Nevertheless, abdominal, thoracic, lymphatic and neurologic complications are the price that is paid by these patients. Our review focuses on Fontan-associated liver disease; the purpose is to summarize the current understanding of its physiopathology, the aim of follow-up and the specific radiologic follow-up performed in Europe. Finally, we as members of the Abdominal Task Force of the European Society of Paediatric Radiology propose a consensus-based imaging follow-up algorithm.
AB - Since Francis Fontan first introduced the eponymous technique, the Fontan procedure, this type of surgical palliation has allowed thousands of children affected by specific heart malformations to reach adulthood. Nevertheless, abdominal, thoracic, lymphatic and neurologic complications are the price that is paid by these patients. Our review focuses on Fontan-associated liver disease; the purpose is to summarize the current understanding of its physiopathology, the aim of follow-up and the specific radiologic follow-up performed in Europe. Finally, we as members of the Abdominal Task Force of the European Society of Paediatric Radiology propose a consensus-based imaging follow-up algorithm.
KW - Adolescents
KW - Children
KW - Cirrhosis
KW - Fontan procedure
KW - Hepatocellular carcinoma
KW - Liver
KW - Liver fibrosis
KW - Magnetic resonance imaging
KW - Ultrasound
UR - http://www.scopus.com/inward/record.url?scp=85117138498&partnerID=8YFLogxK
U2 - https://doi.org/10.1007/s00247-021-05173-x
DO - https://doi.org/10.1007/s00247-021-05173-x
M3 - Article
C2 - 34654967
SN - 0301-0449
VL - 51
SP - 2598
EP - 2606
JO - Pediatric Radiology
JF - Pediatric Radiology
IS - 13
ER -